Yıl 2018, Cilt 11, Sayı 2, Sayfalar 173 - 177 2018-05-14

A rare cause of central cyanosis of newborn: Methemoglobinemia.
Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi

Tuba Leman Karakurt [1]

47 93

Cyanosis is blue-gray appearance of skin, nail bed or mucous membranes that occurs due to non-physiological disorders of hemoglobin or disorders involving deoxygenated hemoglobin. Cyanosis of newborn detected in the first hours of life following delivery is usually associated with pulmonary or cardiac diseases. However, other rare causes also has to be kept in mind in differential diagnosis. One of them is methemoglobinemia. Methemoglobinemia is a serious hemathologic disease results from oxidation of ferrous iron to ferric iron and causes inadequate oxygen transport to tissues and characterized with cyanosis. We report two cases who were hospitalized within the few hours after delivery due to cyanosis and diagnosed as acquired methemoglobinemia. Cases diagnosed as acquired methemoglobinemia caused by maternal pudendal anesthesia were treated successfully with intravenous methylen blue.

İngilizce Kısa Başlık: Central cyanosis of newborn: Methemoglobinemia


Siyanoz; deri, tırnak yatağı veya mukozaların mavimsi gri görünümüdür ve fizyolojik olmayan hemoglobin varlığı ya da deoksijenize hemoglobin düzeyinin yüksekliği zemininde gözlenir.Yenidoğanda doğumu takiben ilk saatlerde ortaya çıkan siyanozun nedeni genellikle kardiyak ya da pulmoner hastalıklardır. Ancak ayırıcı tanıda daha nadir görülen nedenler de akılda tutulmalıdır.Bu tanılardan biri methemoglobinemidir. Methemoglobinemi;ferröz demirin ferrik demire oksitlenmesi sonucu oluşan ve dokulara yetersiz oksijen transferine neden olan, siyanoz ile karakterize, ciddi bir hematolojik hastalıktır. Makalemizde hastanemizde doğumdan sonra saatler içinde gelişen santral siyanoz nedeniyle yatırılan ve edinsel methemoglobinemi tanısı alan iki olgu sunuldu. Maternal pudendal anestezi nedeni ile gelişen edinsel methemoglobinemi vakaları intravenöz metilen mavisi ile başarılı bir şekilde tedavi edilmiştir.

Türkçe Kısa Başlık: Yenidoğanda santral siyanozun nadir nedeni: Methemoglobinemi



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Yazar: Tuba Leman Karakurt (Sorumlu Yazar)
Kurum: Gaziosmanpaşa Taksim Eğitim Araştırma Hastanesi Pediatri, İstanbul
Ülke: Turkey


Bibtex @olgu sunumu { patd399565, journal = {Pamukkale Tıp Dergisi}, issn = {}, eissn = {1308-0865}, address = {Pamukkale Üniversitesi}, year = {2018}, volume = {11}, pages = {173 - 177}, doi = {10.5505/ptd.2018.54771}, title = {Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi}, key = {cite}, author = {Karakurt, Tuba Leman} }
APA Karakurt, T . (2018). Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi. Pamukkale Tıp Dergisi, 11 (2), 173-177. DOI: 10.5505/ptd.2018.54771
MLA Karakurt, T . "Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi". Pamukkale Tıp Dergisi 11 (2018): 173-177 <http://dergipark.gov.tr/patd/issue/36986/399565>
Chicago Karakurt, T . "Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi". Pamukkale Tıp Dergisi 11 (2018): 173-177
RIS TY - JOUR T1 - Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi AU - Tuba Leman Karakurt Y1 - 2018 PY - 2018 N1 - doi: 10.5505/ptd.2018.54771 DO - 10.5505/ptd.2018.54771 T2 - Pamukkale Tıp Dergisi JF - Journal JO - JOR SP - 173 EP - 177 VL - 11 IS - 2 SN - -1308-0865 M3 - doi: 10.5505/ptd.2018.54771 UR - http://dx.doi.org/10.5505/ptd.2018.54771 Y2 - 2018 ER -
EndNote %0 Pamukkale Tıp Dergisi Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi %A Tuba Leman Karakurt %T Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi %D 2018 %J Pamukkale Tıp Dergisi %P -1308-0865 %V 11 %N 2 %R doi: 10.5505/ptd.2018.54771 %U 10.5505/ptd.2018.54771
ISNAD Karakurt, Tuba Leman . "Yenidoğanda gelişen santral siyanozun nadir bir nedeni: Methemoglobinemi". Pamukkale Tıp Dergisi 11 / 2 (Mayıs 2018): 173-177. http://dx.doi.org/10.5505/ptd.2018.54771