Yıl 2018, Cilt 16, Sayı 1, Sayfalar 115 - 124 2018-04-01

Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu

Burcu Tahire Köksal [1] , Özlem Yılmaz Özbek [2] , Esra Özmen [3] , Merih Tepeoğlu [4]

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Stevens-Johnson sendromu (SJS) nadir görülen fakat hayatı tehdit edebilen mukokutanöz tutulumun olduğu T hücre aracılı bir aşırı duyarlılık reaksiyonudur. Olguların çoğu ilaçlarla tetiklenmektedir. Enfeksiyonlar, aşılar, kimyasallar, sistemik ve malign hastalıklar da etiyolojide rol alabilir. Hastalık genellikle ateş, halsizlik, başağrısı, miyalji, artralji ve üst solunum yolu enfeksiyonu gibi prodromal semptomlarla başlar. Stevens-Johnson sendromu için özel bir tedavi yöntemi bulunmamaktadır. Hastalık tanısının hızla konması, sebep olan ilacın erken dönemde kesilmesi ve destek tedavisi tedavinin temelini oluşturmaktadır. Sistemik steroid, intravenöz immünglobulin (IVIG) ve siklosporin gibi ilaçlar da tedavi amacıyla kullanılmaktadır. Stevens-Johnson sendromu farkındalığını arttırmak, erken tanı ve destek tedavinin önemini vurgulamak amacıyla SJS tanısı alan bir olgu sunulmuştur.

ABSTRACT Stevens-Johnson syndrome (SJS) is a rare but life-threatening, mucocutaneous, T cell mediated hypersensitivity reaction. Most of the cases are triggered by a drug. Infections, vaccines, chemicals, systemic or malign diseases may have also roles in etiology. Disease generally starts with prodromal symptoms including fever, malaise, headache, myalgia or upper respiratory tract infection. There is no specific treatment modality for SJS. Diagnosing the disease rapidly, discontinuation of the suspected drug immediately, and supportive therapy are the main steps in treatment. Medications like systemic steroids, intravenous immunglobulin (IVIG) and cyclosporin are also used in treatment. Our aim in presenting a case of SJS is to increase awareness of this disease, to emphasize importance of immediate diagnosis and supportive therapy.

Çocuk, IVIG, parasetamol, Stevens Johnson Sendromu
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Birincil Dil tr
Konular
Dergi Bölümü Olgu
Yazarlar

Yazar: Burcu Tahire Köksal
Kurum: Başkent Üniversitesi Tıp Fakültesi
Ülke: Turkey


Yazar: Özlem Yılmaz Özbek
Kurum: Başkent Üniversitesi Tıp Fakültesi
Ülke: Turkey


Yazar: Esra Özmen
Kurum: Başkent Üniversitesi Tıp Fakültesi
Ülke: Turkey


Yazar: Merih Tepeoğlu
Kurum: Başkent Üniversitesi Tıp Fakültesi
Ülke: Turkey


Bibtex @olgu sunumu { pediatri411400, journal = {Güncel Pediatri}, issn = {1304-9054}, eissn = {1308-6308}, address = {Uludağ Üniversitesi}, year = {2018}, volume = {16}, pages = {115 - 124}, doi = {}, title = {Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu}, key = {cite}, author = {Yılmaz Özbek, Özlem and Tepeoğlu, Merih and Özmen, Esra and Köksal, Burcu Tahire} }
APA Köksal, B , Yılmaz Özbek, Ö , Özmen, E , Tepeoğlu, M . (2018). Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu. Güncel Pediatri, 16 (1), 115-124. Retrieved from http://dergipark.gov.tr/pediatri/issue/36190/411400
MLA Köksal, B , Yılmaz Özbek, Ö , Özmen, E , Tepeoğlu, M . "Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu". Güncel Pediatri 16 (2018): 115-124 <http://dergipark.gov.tr/pediatri/issue/36190/411400>
Chicago Köksal, B , Yılmaz Özbek, Ö , Özmen, E , Tepeoğlu, M . "Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu". Güncel Pediatri 16 (2018): 115-124
RIS TY - JOUR T1 - Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu AU - Burcu Tahire Köksal , Özlem Yılmaz Özbek , Esra Özmen , Merih Tepeoğlu Y1 - 2018 PY - 2018 N1 - DO - T2 - Güncel Pediatri JF - Journal JO - JOR SP - 115 EP - 124 VL - 16 IS - 1 SN - 1304-9054-1308-6308 M3 - UR - Y2 - 2016 ER -
EndNote %0 Güncel Pediatri Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu %A Burcu Tahire Köksal , Özlem Yılmaz Özbek , Esra Özmen , Merih Tepeoğlu %T Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu %D 2018 %J Güncel Pediatri %P 1304-9054-1308-6308 %V 16 %N 1 %R %U
ISNAD Köksal, Burcu Tahire , Yılmaz Özbek, Özlem , Özmen, Esra , Tepeoğlu, Merih . "Stevens Johnson Sendromu Tanısı Alan Bir Çocuk Olgu". Güncel Pediatri 16 / 1 (Nisan 2018): 115-124.