Yıl 2013, Cilt 20, Sayı 3, Sayfalar 111 - 114 2013-10-22

Association of omphalocele and craniorachischisis totalis: The role of three-dimensional ultrasonography with diagnostic features

Kahraman Ülker [1] , İsmail Temur [2] , İnanç Erdoğan [3] , İslim Volkan [4] , Mehmet Karaca [5] , Abdülaziz Gül [6]

153 467

Omphalocele is an anterior abdominal wall defect with the herniation of the visceral contents covered by athin membrane. It is one of the most common malformations of the anterior abdominal wall, with highmorbidity and mortality. The incidence of omphalocele is nearly 1 in 5,000 live births. Cranirachischisistotalis is anencephaly with a contiguous spinal defect. The defect occurs with the failure of neural tube toclose within 28 days after conception and leads to fetal loss, still birth, or neonatal death. Prenatal diagnostictool for both anomalies is ultrasound. In most cases two-dimensional conventional ultrasound providessufficient images for the accurate diagnosis. In this report, we present the association of omphalocele andcraniorachischisis with the three-dimensional ultrasonographic and post-abortal findings
Özet Omfalosel; karın içireğinin ince bir membran içinde fıtıklaştığı karın ön duvarı defektlerindendir. Yüksek morbidite ve mortalite gösteren omfaloselen sık görülen karın ön duvarı defetlerindendir. İnsidansı yaklaşık olarak 5000 canlı doğumda 1'dir. Kranioraşişiz totalis; spinal defektle devamlılık gösteren anensefalidir. Defekt konsepsiyon sonrası 28 günlük sürede nöral tüpün kapanmaması ile oluşur ve fetal kayıp, ölü doğum ya da yenidoğan ölümüyle sonuçlanır. Prenatal tanısal araç iki anomali için de ultrasonografidir. Çoğu vakada iki-boyutlu konvansiyonal ultrasonografi kesin tanı için yeterli görüntüler sağlar. Bu raporda omfalosel ve kranioraşişiz totalis birlikteliğini üç-boyutlu ultrasonografik ve post-abortal bulgularıyla sunuyoruz. Abstract Omphalocele is an anterior abdominal wall defect with the herniation of the visceral contents covered by a thin membrane. It is one of the most common malformations of the anterior abdominal wall, with high morbidity and mortality. The incidence of omphalocele is nearly 1 in 5,000 live births. Cranirachischisis totalis is anencephaly with a contiguous spinal defect. The defect occurs with the failure of neural tube to close within 28 days after conception and leads to fetal loss, still birth, or neonatal death. Prenatal diagnostic tool for both anomalies is ultrasound. In most cases two-dimesional conventional ultrasound provides sufficient images for the accurate diagnosis. In this report, we present the association of omphalocele and craniorachischisis with the three-dimensional ultrasonographic and post-abortal findings.
Omfalosel, Anensefali, Prenatal taný, Karýn ön duvarý defektleri, üç boyutlu görüntü
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Birincil Dil en
Konular
Dergi Bölümü Olgu Sunumları
Yazarlar

Yazar: Kahraman Ülker

Yazar: İsmail Temur

Yazar: İnanç Erdoğan

Yazar: İslim Volkan

Yazar: Mehmet Karaca

Yazar: Abdülaziz Gül

Bibtex
APA Ülker, K , Temur, İ , Erdoğan, İ , Volkan, İ , Karaca, M , Gül, A . (). . , 20 (3), 111-114. Retrieved from http://dergipark.gov.tr/sdutfd/issue/21014/225853
MLA Ülker, K , Temur, İ , Erdoğan, İ , Volkan, İ , Karaca, M , Gül, A . "". 20 (): 111-114 <http://dergipark.gov.tr/sdutfd/issue/21014/225853>
Chicago Ülker, K , Temur, İ , Erdoğan, İ , Volkan, İ , Karaca, M , Gül, A . "". 20 (): 111-114
RIS TY - JOUR T1 - AU - Kahraman Ülker , İsmail Temur , İnanç Erdoğan , İslim Volkan , Mehmet Karaca , Abdülaziz Gül Y1 - 2013 PY - 2013 N1 - DO - T2 - SDÜ Tıp Fakültesi Dergisi JF - Journal JO - JOR SP - 111 EP - 114 VL - 20 IS - 3 SN - 1300-7416-2602-2109 M3 - UR - Y2 - 2018 ER -
EndNote %0 SDÜ Tıp Fakültesi Dergisi %A Kahraman Ülker , İsmail Temur , İnanç Erdoğan , İslim Volkan , Mehmet Karaca , Abdülaziz Gül %T %D 2013 %J SDÜ Tıp Fakültesi Dergisi %P 1300-7416-2602-2109 %V 20 %N 3 %R %U
ISNAD Ülker, Kahraman , Temur, İsmail , Erdoğan, İnanç , Volkan, İslim , Karaca, Mehmet , Gül, Abdülaziz . "Association of omphalocele and craniorachischisis totalis: The role of three-dimensional ultrasonography with diagnostic features". SDÜ Tıp Fakültesi Dergisi 20 / 3 (Ekim 2013): 111-114.